Lymphoproliferative disease and autoimmunity in mice with increased miR-17-92 expression in lymphocytes

Nat Immunol. 2008 Apr;9(4):405-14. doi: 10.1038/ni1575. Epub 2008 Mar 9.

Abstract

The genomic region encoding the miR-17-92 microRNA (miRNA) cluster is often amplified in lymphoma and other cancers, and cancer cells carrying this amplification have higher expression of miRNA in this cluster. Retroviral expression of miR-17-92 accelerates c-Myc-induced lymphoma development, but precisely how higher expression of miR-17-92 promotes lymphomagenesis remains unclear. Here we generated mice with higher expression of miR-17-92 in lymphocytes. These mice developed lymphoproliferative disease and autoimmunity and died prematurely. Lymphocytes from these mice showed more proliferation and less activation-induced cell death. The miR-17-92 miRNA suppressed expression of the tumor suppressor PTEN and the proapoptotic protein Bim. This mechanism probably contributed to the lymphoproliferative disease and autoimmunity of miR-17-92-transgenic mice and contributes to lymphoma development in patients with amplifications of the miR-17-92 coding region.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Autoimmune Diseases / genetics*
  • Autoimmune Diseases / pathology
  • Cell Death / genetics
  • Cell Death / immunology
  • Cell Proliferation
  • Cells, Cultured
  • Gene Amplification
  • Gene Expression Regulation, Neoplastic / immunology
  • Humans
  • Jurkat Cells
  • Lymphocyte Activation / genetics
  • Lymphocyte Activation / immunology
  • Lymphocytes / immunology*
  • Lymphocytes / metabolism
  • Lymphoma / genetics
  • Lymphoma / immunology
  • Lymphoproliferative Disorders / genetics*
  • Lymphoproliferative Disorders / immunology*
  • Lymphoproliferative Disorders / pathology
  • Mice
  • Mice, Inbred C57BL
  • Mice, Transgenic
  • MicroRNAs / biosynthesis*
  • MicroRNAs / genetics*
  • MicroRNAs / physiology

Substances

  • MIRN17 microRNA, human
  • MicroRNAs