[Protracted course of polychondritis as the etiology of progressive nose deformity, subglottic tracheal stenosis and inner ear hearing loss]

Laryngorhinootologie. 1997 Jan;76(1):46-9. doi: 10.1055/s-2007-997385.
[Article in German]

Abstract

Background: Relapsing polychondritis is a rare recurring inflammatory disorder with variable clinical course. Its etiopathogenesis is unknown, but autoimmune mechanisms are likely to be involved.

Patient: We present a case report of a 42-year-old woman with polychondritis manifested in very slowly progressing destruction of the nasal cartilage, additional subglottic tracheal stenosis, and increasing cochlear dysfunction.

Result: We describe and document by a series of photographs the very protracted course of the disease in this patient from early youth until now. Clinical signs and differential diagnosis in polychondritis are discussed.

Conclusion: An early diagnosis in slowly progressing cases like this has to be established in order to permit adequate use of glucocorticoids and/or immunosuppressive drugs, to check the progress of the disease and prevent potentially lethal complications.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Cartilage Diseases / complications*
  • Cartilage Diseases / diagnosis
  • Diagnosis, Differential
  • Female
  • Follow-Up Studies
  • Hearing Loss, Sensorineural / etiology*
  • Humans
  • Nose Deformities, Acquired / etiology*
  • Tracheal Stenosis / etiology*