Fatty acid synthase inhibition alleviates lung fibrosis via β-catenin signal in fibroblasts

Life Sci Alliance. 2024 Nov 20;8(2):e202402805. doi: 10.26508/lsa.202402805. Print 2025 Feb.

Abstract

Idiopathic pulmonary fibrosis is a progressive and lethal interstitial lung disease with an unclear etiology and limited treatment options. Fatty acid synthase (FASN) plays various roles in metabolic-related diseases. This study demonstrates that FASN expression is increased in fibroblasts from the lung tissues of patients with idiopathic pulmonary fibrosis and in bleomycin-treated mice. In MRC-5 cells, the inhibition of FASN using shRNA or the pharmacological inhibitor C75 resulted in the increased mRNA and protein expression of glycogen synthase kinase 3β and Axin1, both negative regulators of the Wnt/β-catenin signaling pathway, and promoted autophagy. This outcome led to a decrease in β-catenin protein and mRNA levels, effectively inhibiting the proliferation, migration, and differentiation of lung fibroblasts into myofibroblasts, while inducing the differentiation of fibroblasts into adipofibroblasts. In vivo experiments showed that C75 alleviated bleomycin-induced lung fibrosis in mice by inhibiting β-catenin. In conclusion, these findings suggest that inhibiting FASN in fibroblasts may diminish the activity of the Wnt/β-catenin signaling pathway, providing a potential therapeutic avenue for pulmonary fibrosis.

MeSH terms

  • Animals
  • Autophagy / drug effects
  • Axin Protein / genetics
  • Axin Protein / metabolism
  • Bleomycin* / adverse effects
  • Cell Differentiation / drug effects
  • Cell Line
  • Cell Movement / drug effects
  • Cell Proliferation / drug effects
  • Fatty Acid Synthases / antagonists & inhibitors
  • Fatty Acid Synthases / metabolism
  • Female
  • Fibroblasts* / drug effects
  • Fibroblasts* / metabolism
  • Glycogen Synthase Kinase 3 beta / metabolism
  • Humans
  • Idiopathic Pulmonary Fibrosis / chemically induced
  • Idiopathic Pulmonary Fibrosis / drug therapy
  • Idiopathic Pulmonary Fibrosis / metabolism
  • Idiopathic Pulmonary Fibrosis / pathology
  • Lung / drug effects
  • Lung / metabolism
  • Lung / pathology
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Myofibroblasts / metabolism
  • Pulmonary Fibrosis / chemically induced
  • Pulmonary Fibrosis / drug therapy
  • Pulmonary Fibrosis / metabolism
  • Pulmonary Fibrosis / pathology
  • Wnt Signaling Pathway* / drug effects
  • beta Catenin* / metabolism

Substances

  • beta Catenin
  • Bleomycin
  • Axin Protein
  • Glycogen Synthase Kinase 3 beta
  • Fatty Acid Synthases
  • AXIN1 protein, human