[Rehabilitation and outcomes in acquired hemophilia A: a single-center clinical study]

Rinsho Ketsueki. 2024;65(10):1270-1275. doi: 10.11406/rinketsu.65.1270.
[Article in Japanese]

Abstract

The main goals of acquired hemophilia A (AHA) therapy are to arrest bleeding using bypass agents and eradicate FVIII inhibitors using immunosuppressive therapy (IST). We treated a total of 25 patients with AHA in the past 10 years at Gunma University Hospital. Fifteen patients (60%) underwent rehabilitation during hospitalization. The median time from admission to the start of rehabilitation was 31 days (7-142 days). Median FVIII activity at the start of rehabilitation was 11.3% (2.9-79.8%), and median FVIII inhibitor was 2.1 BU/ml (<5.0-46.8 BU/ml). Only one patient (6.7%) had a bleeding event triggered by rehabilitation.

Keywords: Acquired hemophilia A; Factor VIII inhibitors; Rehabilitation.

Publication types

  • English Abstract

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Factor VIII / therapeutic use
  • Female
  • Hemophilia A* / rehabilitation
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Male
  • Middle Aged
  • Treatment Outcome

Substances

  • Factor VIII
  • Immunosuppressive Agents

Supplementary concepts

  • Factor 8 deficiency, acquired