Epitope Spreading in Immune-Mediated Glomerulonephritis: The Expanding Target

Int J Mol Sci. 2024 Oct 16;25(20):11096. doi: 10.3390/ijms252011096.

Abstract

Epitope spreading is a critical mechanism driving the progression of autoimmune glomerulonephritis. This phenomenon, where immune responses broaden from a single epitope to encompass additional targets, contributes to the complexity and severity of diseases such as membranous nephropathy (MN), lupus nephritis (LN), and ANCA-associated vasculitis (AAV). In MN, intramolecular spreading within the phospholipase A2 receptor correlates with a worse prognosis, while LN exemplifies both intra- and intermolecular spreading, exacerbating renal involvement. Similarly, ANCA reactivity in AAV highlights the destructive potential of epitope diversification. Understanding these immunological cascades reveals therapeutic opportunities-targeting early epitope spreading could curb disease progression. Despite promising insights, the clinical utility of epitope spreading as a prognostic tool remains debated. This review provides a complete overview of the current evidence, exploring the dual-edged nature of epitope spreading, the intricate immune mechanisms behind it, and its therapeutic implications. By elucidating these dynamics, we aim to pave the way for more precise, targeted interventions in autoimmune glomerular diseases.

Keywords: autoimmune glomerulonephritis; epitope spreading; epitope-specific immune response; glomerular disease progression; targeted immunotherapy.

Publication types

  • Review

MeSH terms

  • Animals
  • Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis / immunology
  • Autoantibodies / immunology
  • Autoimmune Diseases / immunology
  • Epitopes* / immunology
  • Glomerulonephritis* / immunology
  • Glomerulonephritis, Membranous / immunology
  • Humans
  • Lupus Nephritis / immunology
  • Receptors, Phospholipase A2 / immunology

Substances

  • Epitopes
  • Autoantibodies
  • Receptors, Phospholipase A2

Grants and funding

This research received no external funding.