[Primary pulmonary myxoid sarcoma with EWSR1 fusion negative: report of a case]

Zhonghua Bing Li Xue Za Zhi. 2024 Sep 8;53(9):962-964. doi: 10.3760/cma.j.cn112151-20240125-00064.
[Article in Chinese]

Abstract

肺原发性黏液肉瘤是肺部间叶源性肿瘤的罕见类型之一,它的组织学特征和分子学改变较特殊,病理科医师对其准确地认识和辨别是诊断该病的关键。本文报道1例EWSR1融合阴性的肺原发性黏液肉瘤,探讨其临床病理特征,以提高对该疾病的认识。.

Publication types

  • Case Reports

MeSH terms

  • Female
  • Humans
  • Lung Neoplasms* / genetics
  • Lung Neoplasms* / pathology
  • Lung Neoplasms* / surgery
  • Male
  • Middle Aged
  • Myxosarcoma / genetics
  • Myxosarcoma / pathology
  • Myxosarcoma / surgery
  • Oncogene Proteins, Fusion / genetics
  • RNA-Binding Protein EWS* / genetics

Substances

  • RNA-Binding Protein EWS
  • EWSR1 protein, human
  • Oncogene Proteins, Fusion