PKR activation-induced mitochondrial dysfunction in HIV-transgenic mice with nephropathy

Elife. 2024 Aug 29:12:RP91260. doi: 10.7554/eLife.91260.

Abstract

HIV disease remains prevalent in the USA and chronic kidney disease remains a major cause of morbidity in HIV-1-positive patients. Host double-stranded RNA (dsRNA)-activated protein kinase (PKR) is a sensor for viral dsRNA, including HIV-1. We show that PKR inhibition by compound C16 ameliorates the HIV-associated nephropathy (HIVAN) kidney phenotype in the Tg26 transgenic mouse model, with reversal of mitochondrial dysfunction. Combined analysis of single-nucleus RNA-seq and bulk RNA-seq data revealed that oxidative phosphorylation was one of the most downregulated pathways and identified signal transducer and activator of transcription (STAT3) as a potential mediating factor. We identified in Tg26 mice a novel proximal tubular cell cluster enriched in mitochondrial transcripts. Podocytes showed high levels of HIV-1 gene expression and dysregulation of cytoskeleton-related genes, and these cells dedifferentiated. In injured proximal tubules, cell-cell interaction analysis indicated activation of the pro-fibrogenic PKR-STAT3-platelet-derived growth factor (PDGF)-D pathway. These findings suggest that PKR inhibition and mitochondrial rescue are potential novel therapeutic approaches for HIVAN.

Keywords: HIV; HIV-associated nephropathy; RNA-seq; medicine; mitochondria; mouse; protein kinase R; single-nucleus RNA-seq.

MeSH terms

  • AIDS-Associated Nephropathy* / genetics
  • AIDS-Associated Nephropathy* / metabolism
  • AIDS-Associated Nephropathy* / pathology
  • Animals
  • Disease Models, Animal
  • HIV-1 / genetics
  • HIV-1 / physiology
  • Humans
  • Mice
  • Mice, Transgenic*
  • Mitochondria* / metabolism
  • Podocytes / metabolism
  • STAT3 Transcription Factor / genetics
  • STAT3 Transcription Factor / metabolism
  • eIF-2 Kinase* / genetics
  • eIF-2 Kinase* / metabolism

Substances

  • eIF-2 Kinase
  • protein kinase R, mouse
  • STAT3 Transcription Factor

Associated data

  • GEO/GSE205060
  • GEO/GSE131882
  • GEO/GSE139107