p38γ/δ activation alters cardiac electrical activity and predisposes to ventricular arrhythmia

Nat Cardiovasc Res. 2023 Dec;2(12):1204-1220. doi: 10.1038/s44161-023-00368-x. Epub 2023 Nov 27.

Abstract

Ventricular fibrillation (VF) is a leading immediate cause of sudden cardiac death. There is a strong association between aging and VF, although the mechanisms are unclear, limiting the availability of targeted therapeutic interventions. Here we found that the stress kinases p38γ and p38δ are activated in the ventricles of old mice and mice with genetic or drug-induced arrhythmogenic conditions. We discovered that, upon activation, p38γ and p38δ cooperatively increase the susceptibility to stress-induced VF. Mechanistically, our data indicate that activated p38γ and p38δ phosphorylate ryanodine receptor 2 (RyR2) disrupt Kv4.3 channel localization, promoting sarcoplasmic reticulum calcium leak, Ito current reduction and action potential duration prolongation. In turn, this led to aberrant intracellular calcium handling, premature ventricular complexes and enhanced susceptibility to VF. Blocking this pathway protected genetically modified animals from VF development and reduced the VF duration in aged animals. These results indicate that p38γ and p38δ are a potential therapeutic target for sustained VF prevention.

MeSH terms

  • Action Potentials / drug effects
  • Action Potentials / physiology
  • Age Factors
  • Animals
  • Calcium Signaling
  • Disease Models, Animal
  • Enzyme Activation
  • Humans
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Mitogen-Activated Protein Kinase 12* / genetics
  • Mitogen-Activated Protein Kinase 12* / metabolism
  • Mitogen-Activated Protein Kinase 13 / genetics
  • Mitogen-Activated Protein Kinase 13 / metabolism
  • Myocytes, Cardiac / metabolism
  • Phosphorylation
  • Ryanodine Receptor Calcium Release Channel* / genetics
  • Ryanodine Receptor Calcium Release Channel* / metabolism
  • Sarcoplasmic Reticulum / metabolism
  • Ventricular Fibrillation* / genetics
  • Ventricular Fibrillation* / metabolism
  • Ventricular Fibrillation* / physiopathology
  • Ventricular Premature Complexes / genetics
  • Ventricular Premature Complexes / metabolism
  • Ventricular Premature Complexes / physiopathology

Substances

  • Mitogen-Activated Protein Kinase 12
  • Ryanodine Receptor Calcium Release Channel
  • Mitogen-Activated Protein Kinase 13
  • ryanodine receptor 2. mouse