Treatment of idiopathic nephrotic syndrome at onset: a comparison between 8- and 12-week regimens in everyday clinical practice

Pediatr Nephrol. 2023 Jul;38(7):2101-2106. doi: 10.1007/s00467-022-05824-7. Epub 2022 Nov 24.

Abstract

Background: Optimal steroid treatment at onset of idiopathic nephrotic syndrome is still debated. The aim of this study was to analyze the clinical outcome at 24 months of follow-up in patients admitted to our unit for the first episode of steroid-sensitive nephrotic syndrome comparing two different steroid regimens.

Methods: We collected data on patients treated from 1992 to 2007 with prednisone according to the International Study on Kidney Diseases in Children 8-week regimen and since 2008 according to the Arbeitsgemeinschaft fur Padiatrische Nephrologie 12-week regimen. The primary outcome was to evaluate cumulative prednisone dosage at 12 and 24 months of follow-up in the two groups. As secondary outcomes, we considered mean relapse rate per patient; number of children without relapses at 6, 12, and 24 months; and number of patients who developed frequent relapses and steroid-dependent disease.

Results: Data were collected on 127 patients. Sixty-one subjects received the 8-week regimen and 66 the 12-week regimen. The mean cumulative prednisone dose at 12 and 24 months was not different, and the rate of patients without relapses was lower at 6 and 12 months in patients treated with the 8-week course, while no difference was observed at 24 months.

Conclusions: Despite the limitations of a retrospective study with limited follow-up, our data indicate that switching treatment from a shorter to a longer scheme did not improve the clinical outcome at 24 months of observation. A higher resolution version of the Graphical abstract is available as Supplementary information.

Keywords: Cumulative prednisone dose; Relapse; Steroid treatment; Steroid-sensitive nephrotic syndrome.

MeSH terms

  • Child
  • Humans
  • Nephrosis, Lipoid* / drug therapy
  • Nephrotic Syndrome* / drug therapy
  • Prednisone / adverse effects
  • Recurrence
  • Retrospective Studies

Substances

  • Prednisone

Supplementary concepts

  • Nephrosis, congenital