Structure-activity mapping of ARHGAP36 reveals regulatory roles for its GAP homology and C-terminal domains

PLoS One. 2021 May 17;16(5):e0251684. doi: 10.1371/journal.pone.0251684. eCollection 2021.

Abstract

ARHGAP36 is an atypical Rho GTPase-activating protein (GAP) family member that drives both spinal cord development and tumorigenesis, acting in part through an N-terminal motif that suppresses protein kinase A and activates Gli transcription factors. ARHGAP36 also contains isoform-specific N-terminal sequences, a central GAP-like module, and a unique C-terminal domain, and the functions of these regions remain unknown. Here we have mapped the ARHGAP36 structure-activity landscape using a deep sequencing-based mutagenesis screen and truncation mutant analyses. Using this approach, we have discovered several residues in the GAP homology domain that are essential for Gli activation and a role for the C-terminal domain in counteracting an N-terminal autoinhibitory motif that is present in certain ARHGAP36 isoforms. In addition, each of these sites modulates ARHGAP36 recruitment to the plasma membrane or primary cilium. Through comparative proteomics, we also have identified proteins that preferentially interact with active ARHGAP36, and we demonstrate that one binding partner, prolyl oligopeptidase-like protein, is a novel ARHGAP36 antagonist. Our work reveals multiple modes of ARHGAP36 regulation and establishes an experimental framework that can be applied towards other signaling proteins.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cilia* / chemistry
  • Cilia* / genetics
  • Cilia* / metabolism
  • GTPase-Activating Proteins* / biosynthesis
  • GTPase-Activating Proteins* / chemistry
  • GTPase-Activating Proteins* / genetics
  • HEK293 Cells
  • Humans
  • Mice
  • NIH 3T3 Cells
  • Protein Domains
  • Protein Isoforms
  • Signal Transduction*
  • Structure-Activity Relationship

Substances

  • ARHGAP36 protein, human
  • GTPase-Activating Proteins
  • Protein Isoforms

Associated data

  • Dryad/10.5061/dryad.dz08kprv9