Thrombotic Microangiopathy Following Onasemnogene Abeparvovec for Spinal Muscular Atrophy: A Case Series

J Pediatr. 2021 Apr:231:265-268. doi: 10.1016/j.jpeds.2020.11.054. Epub 2020 Nov 28.

Abstract

Spinal muscular atrophy is treated with onasemnogene abeparvovec, which replaces the missing survival motor neuron 1 gene via an adeno-associated virus vector. As of July 1, 2020, we had identified 3 infants who developed thrombotic microangiopathy following onasemnogene abeparvovec. Early recognition and treatment of drug-induced thrombotic microangiopathy may lessen mortality and morbidity.

Keywords: gene therapy; hemolytic uremic syndrome; safety; survival motor neuron.

Publication types

  • Case Reports

MeSH terms

  • Biological Products / adverse effects*
  • Biological Products / therapeutic use
  • Female
  • Humans
  • Infant
  • Muscular Atrophy, Spinal / drug therapy*
  • Recombinant Fusion Proteins / adverse effects*
  • Recombinant Fusion Proteins / therapeutic use
  • Thrombotic Microangiopathies / chemically induced*

Substances

  • Biological Products
  • Recombinant Fusion Proteins
  • Zolgensma