The World Federation of Hemophilia Annual Global Survey 1999-2018

Haemophilia. 2020 Jul;26(4):591-600. doi: 10.1111/hae.14012. Epub 2020 Jun 4.

Abstract

Introduction: The World Federation of Hemophilia (WFH) strives to achieve care for all patients with inherited bleeding disorders through research, advocacy, capacity building and education. The WFH developed and implemented the Annual Global Survey (AGS), through which comprehensive demographic and treatment data on bleeding disorders are collected each year from its constituent non-governmental national organizations.

Aim: To describe the development, methodology and achievements of the WFH AGS over the past 20 years.

Methods: The AGS is a yearly cross-sectional survey. Data are collected using a standardized form (available online and on paper), quality checked and reviewed, and published in English, French and Spanish. Over time, the AGS has been modified in response to changes in treatment landscape or emerging new issues.

Results: Over the past 20 years, the AGS has reported an increase in the number of countries participating in the survey, a tripling in the number of people identified with rare bleeding disorders and an increase in the amount of factor used to treat people with haemophilia. Yet, a large treatment inequity gap still exists across the globe. In response to this gap, the WFH has analysed the AGS reports which has stimulated further development in quality of care indicators, estimates of the global prevalence of haemophilia, patient-level data collection efforts like the World Bleeding Disorders Registry and the Gene Therapy Registry.

Conclusion: The AGS has provided evidence to support research, programme planning and development activities of the WFH.

Keywords: annual global survey; bleeding disorder; haemophilia; von Willebrand disease.

MeSH terms

  • Adolescent
  • Cross-Sectional Studies / methods*
  • Delivery of Health Care / standards
  • Developing Countries / economics
  • Developing Countries / statistics & numerical data
  • Factor VIII / therapeutic use
  • Female
  • HIV Infections / epidemiology
  • Healthcare Disparities / statistics & numerical data
  • Hemophilia A / diagnosis
  • Hemophilia A / drug therapy*
  • Hemophilia A / epidemiology
  • Hemophilia A / prevention & control
  • Hepatitis C / epidemiology
  • Humans
  • International Cooperation / legislation & jurisprudence*
  • Male
  • Organizations / organization & administration*
  • Prevalence
  • Severity of Illness Index
  • Young Adult
  • von Willebrand Diseases / diagnosis
  • von Willebrand Diseases / epidemiology
  • von Willebrand Diseases / prevention & control

Substances

  • Factor VIII