In adults with congenital heart disease, atrial fibrillation occurs at a lower age due to the increased atrial stress compared to structurally normal hearts. The ablation target thus results from the underlying heart defect and the specific arrhythmia: in the case of atrial fibrillation, pulmonary vein isolation with left atrial substrate modification can be performed safely and effectively taking into account the individual cardiac lesion, which is often related to difficult transseptal access. This case is a representative example of catheter ablation of atrial fibrillation in a patient with a functional univentricular heart using intracardiac echocardiography-guided double transseptal puncture.
Keywords: ACHD; Adults with congenital heart disease; Intracardiac echocardiography; Pulmonary atresia; Pulmonary vein isolation.