Neonatal vesiculopustular eruption in Down syndrome and transient myeloproliferative disorder: A case report and review of the literature

Pediatr Dermatol. 2019 Sep;36(5):702-706. doi: 10.1111/pde.13931. Epub 2019 Jul 29.

Abstract

Transient myeloproliferative disorder (TMD) is a spontaneously resolving clonal myeloid proliferation characterized by circulating megakaryoblasts in the peripheral blood that is restricted to neonates with Down syndrome (DS) or those with trisomy 21 mosaicism. Cutaneous manifestations of TMD are observed in only 5% of affected neonates and present as a diffuse eruption of erythematous, crusted papules, papulovesicles, and pustules, often with prominent and initial facial involvement. We describe the case of a male infant with DS and TMD, associated with a vesiculopustular eruption, which appeared on day 36 of life, and review previous cases.

Keywords: Down syndrome; neonatal vesiculopustular eruption; transient myeloproliferative disorder; trisomy 21.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Down Syndrome / complications*
  • Down Syndrome / pathology
  • Humans
  • Infant, Newborn
  • Leukemoid Reaction / complications*
  • Leukemoid Reaction / pathology
  • Male
  • Skin Diseases, Vesiculobullous / etiology*
  • Skin Diseases, Vesiculobullous / pathology

Supplementary concepts

  • Myeloproliferative Syndrome, Transient