Pituitary carcinomas: review of the current literature and report of atypical case

Br J Neurosurg. 2020 Oct;34(5):528-533. doi: 10.1080/02688697.2019.1582750. Epub 2019 Mar 5.

Abstract

Introduction: Pituitary carcinomas are poorly understood, rare entities. They are distinguished from adenomas not by histopathological features but rather by the presence of metastases.Objective: We discuss the diagnosis, mechanism of dissemination and pathogenesis based on a review of the literature and illustrated by a singular case.Case Report: A 59-year-old male presented with a dural-based posterior fossa lesion. He had been diagnosed with a pituitary chromophobe adenoma 43 years earlier that was treated at the time with surgery and radiation therapy. A presumptive diagnosis of a radiation-induced meningioma was made and surgery was recommended. At surgery the tumour resembled a pituitary adenoma. Histopathology, laboratory findings, and the patient's medical history confirmed the final diagnosis of a prolactin-secreting pituitary carcinoma. To our knowledge, this is the longest reported interval between the pituitary adenoma and metastatic lesion diagnosis (43 years).Conclusion: Management should be tailored to individual patient and may include a combination of treatments (surgery, radiation therapy, chemotherapy, and hormone-targeted therapy). Functionally active tumours may be monitored with hormone levels as tumour markers.

Keywords: Pituitary Diseases; endocrinology; neurosurgery; pituitary carcinoma; prolactinoma.

Publication types

  • Case Reports

MeSH terms

  • Adenoma* / diagnosis
  • Adenoma* / surgery
  • Humans
  • Male
  • Middle Aged
  • Neoplasms, Radiation-Induced*
  • Pituitary Neoplasms* / diagnostic imaging
  • Pituitary Neoplasms* / surgery