Adult-onset tumour necrosis factor receptor-associated periodic syndrome presenting as transfusion-dependent refractory haemophagocytosis

Rheumatology (Oxford). 2018 Mar 1;57(3):582-583. doi: 10.1093/rheumatology/kex427.

Authors

Taryn Youngstein¹, Mickey B C Koh², Jose Ros Soto², Dorota Rowczenio¹, Hadija Trojer¹, Helen J Lachmann¹, Nidhi Sofat³

Affiliations

¹ National Amyloidosis Centre, UCL Division of Medicine, Royal Free Hospital, London, UK.
² Department of Haematology, St George's University Hospitals NHS Foundation Trust, London, UK.
³ Institute for Infection & Immunity, St George's University of London and Department of Rheumatology, St George's University Hospitals NHS Foundation Trust, London, UK.

PMID: 29228362
DOI: 10.1093/rheumatology/kex427

No abstract available

Publication types

Case Reports
Letter

MeSH terms

Adult
Blood Transfusion / methods
Hereditary Autoinflammatory Diseases / blood
Hereditary Autoinflammatory Diseases / complications*
Humans
Lymphohistiocytosis, Hemophagocytic / immunology*
Lymphohistiocytosis, Hemophagocytic / therapy
Male
Receptors, Tumor Necrosis Factor / blood

Substances

Receptors, Tumor Necrosis Factor