Meis2 as a critical player in MN1-induced leukemia

Blood Cancer J. 2017 Sep 29;7(9):e613. doi: 10.1038/bcj.2017.86.

Abstract

Meningioma 1 (MN1) is an independent prognostic marker for normal karyotype acute myeloid leukemia (AML), with high expression linked to all-trans retinoic acid resistance and poor survival. MN1 is also a potent and sufficient oncogene in murine leukemia models, strongly dependent on the MEIS1/AbdB-like HOX protein complex to transform common myeloid progenitors, block myeloid differentiation, and promote leukemic stem cell self-renewal. To identify key genes and pathways underlying leukemic activity, we functionally assessed MN1 cell phenotypic heterogeneity, revealing leukemic and non-leukemic subsets. Using gene expression profiling of these subsets combined with previously published comparisons of full-length MN1 and mutants with varying leukemogenic activity, we identified candidate genes critical to leukemia. Functional analysis identified Hlf and Hoxa9 as critical to MN1 in vitro proliferation, self-renewal and impaired myeloid differentiation. Although critical to transformation, Meis1 knockdown had little impact on these properties in vitro. However, we identified Meis2 as critical to MN1-induced leukemia, with essential roles in proliferation, self-renewal, impairment of differentiation and disease progression in vitro and in vivo. Here, we provide evidence of phenotypic and functional hierarchy in MN1-induced leukemic cells, characterise contributions of Hlf, Hoxa9 and Meis1 to in vitro leukemic properties, and reveal Meis2 as a novel player in MN1-induced leukemogenesis.

MeSH terms

  • Animals
  • Basic-Leucine Zipper Transcription Factors / genetics
  • Basic-Leucine Zipper Transcription Factors / metabolism
  • Gene Expression Regulation, Leukemic*
  • Gene Knockdown Techniques
  • Homeodomain Proteins / genetics
  • Homeodomain Proteins / metabolism*
  • Leukemia / genetics
  • Leukemia / metabolism*
  • Leukemia / pathology
  • Mice
  • Myeloid Ecotropic Viral Integration Site 1 Protein / genetics
  • Myeloid Ecotropic Viral Integration Site 1 Protein / metabolism
  • Oncogene Proteins / genetics
  • Oncogene Proteins / metabolism*
  • Trans-Activators
  • Tumor Suppressor Proteins

Substances

  • Basic-Leucine Zipper Transcription Factors
  • Hlf protein, mouse
  • Homeodomain Proteins
  • Meis1 protein, mouse
  • Mn1 protein, mouse
  • Mrg1 protein, mouse
  • Myeloid Ecotropic Viral Integration Site 1 Protein
  • Oncogene Proteins
  • Trans-Activators
  • Tumor Suppressor Proteins
  • homeobox protein HOXA9

Grants and funding