Respiratory Complications Lead to the Diagnosis of Chronic Granulomatous Disease in Two Adult Patients

J Clin Immunol. 2017 Feb;37(2):113-116. doi: 10.1007/s10875-017-0370-1. Epub 2017 Jan 27.

Abstract

Chronic granulomatous disease (CGD) is a primary immunodeficiency associated to multiple life-threatening bacterial and fungal infections, beginning in childhood. There are rare cases of diagnosis in adulthood. We describe here two cases of late diagnosis in adults: a 45-year-old woman and 59-year-old-man. CGD diagnosis should be considered in adult patients with unexplained infectious diseases with tissue granuloma.

Keywords: CGD; NCF1; Pantoea; ROS; colitis; inflammatory bowel disease; pulmonary aspergillosis; pulmonary disease.

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Biomarkers
  • Female
  • Granulomatous Disease, Chronic / complications*
  • Granulomatous Disease, Chronic / diagnosis*
  • Humans
  • Male
  • Middle Aged
  • Neutrophils / immunology
  • Neutrophils / metabolism
  • Pulmonary Aspergillosis / diagnosis*
  • Pulmonary Aspergillosis / drug therapy
  • Pulmonary Aspergillosis / etiology*
  • Tomography, X-Ray Computed

Substances

  • Biomarkers