The use of anthracyclines in the treatment of endemic Burkitt lymphoma

Br J Haematol. 2017 Jun;177(6):984-990. doi: 10.1111/bjh.14440. Epub 2016 Nov 28.

Abstract

Burkitt lymphoma is the most common malignancy in children in Malawi, the world's poorest country, where there is a long history of treating this disease using a 28-day cyclophosphamide-based protocol. Stage III/IV disease has had poor outcomes. In an attempt to improve the outcome for higher stage disease, anthracyclines were added to the existing protocol. The disease-free (DFS) and overall survival (OS) of 58 children with cytologically confirmed Burkitt lymphoma admitted during 2012-2014 and treated using this protocol were calculated. Six (10%) children had stage I disease, ten (17%) stage II and 42 stage III or IV (73%). Overall 12-month DFS (OS) was 68·5% (72·9%); for stage I disease 100% (100%), stage II 56·2% (60%), stage III/IV 66·3% (72·2%). The DFS was significantly improved from the previous protocol (P = 8 × 10-4 ). The addition of doxorubicin to stage III and IV disease resulted in a markedly improved DFS. Anthracyclines are deliverable in resource-poor settings and possibly improve the survival of children with Burkitt lymphoma.

Keywords: Burkitt lymphoma; anthracyclines; chemotherapy; endemic; resource-challenged countries.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Anthracyclines / administration & dosage
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use*
  • Burkitt Lymphoma / drug therapy*
  • Burkitt Lymphoma / pathology
  • Child
  • Child, Preschool
  • Doxorubicin / administration & dosage
  • Female
  • Humans
  • Kaplan-Meier Estimate
  • Male
  • Medically Underserved Area
  • Neoplasm Staging

Substances

  • Anthracyclines
  • Doxorubicin