Abnormal B-cell maturation in the bone marrow of patients with germline mutations in PIK3CD

J Allergy Clin Immunol. 2017 Mar;139(3):1032-1035.e6. doi: 10.1016/j.jaci.2016.08.028. Epub 2016 Sep 30.

Abstract

Patients with germline mutations in PIK3CD, immunodeficiency, lymphoproliferation, and autoimmunity show a distinct pattern of abnormal B-cell maturation in the bone marrow.

Publication types

  • Letter
  • Research Support, N.I.H., Extramural
  • Research Support, N.I.H., Intramural

MeSH terms

  • Adolescent
  • B-Lymphocytes / pathology*
  • Bone Marrow Cells / pathology*
  • Cell Differentiation / genetics
  • Cell Differentiation / immunology
  • Child
  • Child, Preschool
  • Class I Phosphatidylinositol 3-Kinases / genetics*
  • Female
  • Germ-Line Mutation
  • Hematologic Diseases / genetics*
  • Humans
  • Male
  • Precursor Cells, B-Lymphoid / pathology
  • Young Adult

Substances

  • Class I Phosphatidylinositol 3-Kinases
  • PIK3CD protein, human