Critical reappraisal confirms that Mitofusin 2 is an endoplasmic reticulum-mitochondria tether

Proc Natl Acad Sci U S A. 2016 Oct 4;113(40):11249-11254. doi: 10.1073/pnas.1606786113. Epub 2016 Sep 19.

Abstract

The discovery of the multiple roles of mitochondria-endoplasmic reticulum (ER) juxtaposition in cell biology often relied upon the exploitation of Mitofusin (Mfn) 2 as an ER-mitochondria tether. However, this established Mfn2 function was recently questioned, calling for a critical re-evaluation of Mfn2's role in ER-mitochondria cross-talk. Electron microscopy and fluorescence-based probes of organelle proximity confirmed that ER-mitochondria juxtaposition was reduced by constitutive or acute Mfn2 deletion. Functionally, mitochondrial uptake of Ca2+ released from the ER was reduced following acute Mfn2 ablation, as well as in Mfn2-/- cells overexpressing the mitochondrial calcium uniporter. Mitochondrial Ca2+ uptake rate and extent were normal in isolated Mfn2-/- liver mitochondria, consistent with the finding that acute or chronic Mfn2 ablation or overexpression did not alter mitochondrial calcium uniporter complex component levels. Hence, Mfn2 stands as a bona fide ER-mitochondria tether whose ablation decreases interorganellar juxtaposition and communication.

Keywords: Ca2+; Mfn2; interorganellar communication; mitochondria; tethering.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Calcium / metabolism
  • Calcium Channels / metabolism
  • Embryo, Mammalian / cytology
  • Endoplasmic Reticulum / metabolism*
  • Endoplasmic Reticulum / ultrastructure
  • Fibroblasts / metabolism
  • Fibroblasts / ultrastructure
  • GTP Phosphohydrolases / metabolism*
  • Gene Deletion
  • Human Umbilical Vein Endothelial Cells / metabolism
  • Humans
  • Liver / metabolism
  • Mice, Knockout
  • Mitochondria / metabolism*
  • Mitochondria / ultrastructure
  • Molecular Probes / metabolism

Substances

  • Calcium Channels
  • Molecular Probes
  • mitochondrial calcium uniporter
  • GTP Phosphohydrolases
  • Mfn2 protein, mouse
  • Calcium