Retinal Vasculitis in Anti-Synthetase Syndrome

Ophthalmic Surg Lasers Imaging Retina. 2016 Sep 1;47(9):874-9. doi: 10.3928/23258160-20160901-13.

Abstract

A 31-year-old woman with a history of anti-synthetase syndrome-related myositis and interstitial lung disease presented with acute-onset blurry vision and rash on her hands and feet. Visual acuity was hand motion in her right eye and 20/40 in her left eye. Dilated fundus exam showed extensive retinal vasculitis, diffuse intraretinal hemorrhages, and subretinal fluid. Optical coherence tomography revealed significant macular thickening, and fluorescein angiography revealed vascular leakage with peripheral nonperfusion. Aggressive systemic immunosuppression was initiated, with gradual resolution of her disease during 8 months of follow-up. [Ophthalmic Surg Lasers Imaging Retina. 2016;47:874-879.].

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Female
  • Fluorescein Angiography / methods*
  • Fundus Oculi
  • Humans
  • Myositis / complications*
  • Myositis / diagnosis
  • Retina / pathology*
  • Retinal Vasculitis / diagnosis
  • Retinal Vasculitis / etiology*
  • Tomography, Optical Coherence / methods*
  • Visual Acuity

Supplementary concepts

  • Antisynthetase syndrome