Mechanosensing by the α6-integrin confers an invasive fibroblast phenotype and mediates lung fibrosis

Nat Commun. 2016 Aug 18:7:12564. doi: 10.1038/ncomms12564.

Abstract

Matrix stiffening is a prominent feature of pulmonary fibrosis. In this study, we demonstrate that matrix stiffness regulates the ability of fibrotic lung myofibroblasts to invade the basement membrane (BM). We identify α6-integrin as a mechanosensing integrin subunit that mediates matrix stiffness-regulated myofibroblast invasion. Increasing α6-expression, specifically the B isoform (α6B), couples β1-integrin to mediate MMP-2-dependent pericellular proteolysis of BM collagen IV, leading to myofibroblast invasion. Human idiopathic pulmonary fibrosis lung myofibroblasts express high levels of α6-integrin in vitro and in vivo. Genetic ablation of α6 in collagen-expressing mesenchymal cells or pharmacological blockade of matrix stiffness-regulated α6-expression protects mice against bleomycin injury-induced experimental lung fibrosis. These findings suggest that α6-integrin is a matrix stiffness-regulated mechanosensitive molecule which confers an invasive fibroblast phenotype and mediates experimental lung fibrosis. Targeting this mechanosensing α6(β1)-integrin offers a novel anti-fibrotic strategy against lung fibrosis.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Basement Membrane / metabolism
  • Basement Membrane / pathology
  • Bleomycin
  • Cell Adhesion
  • Extracellular Matrix / metabolism
  • Fibroblasts / pathology*
  • Gene Deletion
  • Humans
  • Integrin alpha6 / metabolism*
  • Lung / metabolism*
  • Lung / pathology*
  • Mechanotransduction, Cellular* / genetics
  • Mice, Inbred C57BL
  • Models, Biological
  • Myofibroblasts / metabolism
  • Myofibroblasts / pathology
  • Phenotype
  • Proto-Oncogene Proteins c-fos / metabolism
  • Pulmonary Fibrosis / genetics
  • Pulmonary Fibrosis / metabolism*
  • Pulmonary Fibrosis / pathology*
  • Up-Regulation
  • rho-Associated Kinases / metabolism

Substances

  • Integrin alpha6
  • Proto-Oncogene Proteins c-fos
  • Bleomycin
  • rho-Associated Kinases