Differences between familial and sporadic early spondyloarthritis: results from the ESPERANZA cohort

Clin Exp Rheumatol. 2016 Jul-Aug;34(4):575-80. Epub 2016 Jun 22.

Abstract

Objectives: To describe and evaluate clinical and imaging differences between patients with familial and sporadic early spondyloarthritis (SpA).

Methods: This was a cross-sectional study analysing the baseline dataset from ESPERANZA, a national programme developed for the early identification of patients with SpA. Patients fulfilling SpA ASAS classification criteria were included. Familial SpA was defined according to the ASAS/ESSG criteria as the presence in first- or second-degree relatives of any of the following: ankylosing spondylitis, psoriasis, uveitis, reactive arthritis, and inflammatory bowel disease. Socio-demographic and disease characteristics, disease activity, metrology and laboratory and imaging data were compared by descriptive and bivariate statistics.

Results: A total of 377 patients were included - 64% men, mean age 32, and mean disease duration 12 months. Out of these, 132 (35%) patients (101 axial and 31 peripheral SpA) were familial forms. In patients with axial SpA, statistically significant differences (p<0.05) were found between familial and sporadic forms regarding age at symptoms onset (29.4±9.2 vs. 31.5±10 years), HLA B27 positivity (83% vs. 71%), BASMI (1.2± 13 vs. 1.6 1.2) and sacroiliitis on magnetic resonance imaging (36% vs. 47%), respectively. In patients with peripheral SpA, there were no significant differences for any of the variables analysed.

Conclusions: Familial axial SpA presents symptoms at a younger age, is more frequently HLA-B27 positive and shows better spinal mobility than sporadic axial SpA; this latter presenting sacroiliitis on MRI more frequently than familial axial SpA. Apparently, no differences exist in the expression of familial or sporadic peripheral SpA.

Publication types

  • Comparative Study

MeSH terms

  • Adult
  • Age of Onset
  • Cross-Sectional Studies
  • Databases, Factual
  • Early Diagnosis
  • Female
  • Genetic Testing
  • HLA-B27 Antigen / immunology
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Phenotype
  • Predictive Value of Tests
  • Prognosis
  • Risk Factors
  • Spain / epidemiology
  • Spondylarthritis / diagnosis*
  • Spondylarthritis / epidemiology
  • Spondylarthritis / genetics
  • Spondylarthritis / immunology

Substances

  • HLA-B27 Antigen