The thymus and rheumatology: should we care?

Curr Opin Rheumatol. 2016 Mar;28(2):189-95. doi: 10.1097/BOR.0000000000000251.

Abstract

Purpose of review: The purpose of this review is to discuss the mechanisms of central and peripheral tolerance in relation to T-cell mediated autoimmunity in rheumatoid arthritis (RA).

Recent findings: The well established association between major histocompatibility complex class II and RA has led us to understand that T cells, and the adaptive immune response, are important in the pathogenesis of disease. In order for autoimmune disease to develop, there is a breach of tolerance to self antigen and the mechanisms of both central and peripheral tolerance aim to prevent this. Here, we review evidence from mouse models indicating that alterations in T-cell receptor signalling thresholds during thymic selection may be linked to the escape of T cells that mediate autoimmune arthritis. In addition, we summarize the role of dendritic cells and Foxp3+ regulatory T cells in both peripheral and thymic tolerance, and highlight their relevance to what we know about the aetiology of RA.

Summary: Mechanisms of central tolerance in the thymus and peripheral tolerance are in place to control autoreactive T cells and to prevent the development of autoimmune disease. We anticipate that a better understanding of these mechanisms will lead to the development of better, antigen-specific therapeutics to restore tolerance.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Animals
  • Arthritis, Experimental / immunology
  • Arthritis, Rheumatoid / genetics
  • Arthritis, Rheumatoid / immunology*
  • Autoantigens / immunology
  • Autoimmune Diseases / immunology
  • Autoimmunity / immunology
  • Dendritic Cells / immunology
  • Humans
  • Immune Tolerance / immunology
  • Polymorphism, Single Nucleotide
  • Protein Tyrosine Phosphatase, Non-Receptor Type 22 / genetics
  • T-Lymphocytes, Regulatory / immunology
  • Thymus Gland / immunology

Substances

  • Autoantigens
  • PTPN22 protein, human
  • Protein Tyrosine Phosphatase, Non-Receptor Type 22