Pediatric Hemorrhagic Brainstem Encephalitis Associated With HHV-7 Infection

Pediatr Neurol. 2015 Dec;53(6):523-6. doi: 10.1016/j.pediatrneurol.2015.06.016. Epub 2015 Jun 27.

Abstract

Background: Human herpesviruses-6 and -7 have been associated with febrile seizures and with encephalitis, the latter predominantly in immunocompromised individuals. Acute hemorrhagic encephalitis is frequently a fatal disease that can occur in the setting of viral infection or can be a postinfectious phenomenon, often with no cause identified. Although hemorrhagic encephalitis has been reported with human herpesvirus-6 infection, only one individual, an immunocompromised child, has been documented with human herpesvirus-7 infection. The role of immunosuppression is not well-established in the management of this rare condition.

Patient description: We present an 11-year-old boy with hemorrhagic brainstem encephalitis who underwent extensive infectious and autoimmune testing, positive only for human herpesvirus-7 in the cerebrospinal fluid. The patient recovered after treatment with intravenous immunoglobulin, high-dose steroids, and plasma exchange.

Conclusion: This is the first report of hemorrhagic brainstem encephalitis with human herpesvirus-7 in a previously healthy individual, adding to existing reports of late-onset human herpesvirus-7 infection associated with encephalitis in children. It also underscores that aggressive immunosuppression may be used early in the course of this disorder and may be beneficial for recovery.

Keywords: HHV-7; hemorrhagic encephalitis; herpesvirus; pediatric.

Publication types

  • Case Reports

MeSH terms

  • Brain Stem / pathology*
  • Child
  • Encephalitis, Viral / complications*
  • Encephalitis, Viral / diagnosis
  • Herpesvirus 7, Human / pathogenicity*
  • Humans
  • Intracranial Hemorrhages / diagnosis
  • Intracranial Hemorrhages / etiology*
  • Male
  • Roseolovirus Infections / complications*
  • Roseolovirus Infections / diagnosis