Silencing autocrine death: a ubiquitin ligase that blocks activation-induced cell death in cutaneous T-cell lymphoma

J Invest Dermatol. 2015 Mar;135(3):662-665. doi: 10.1038/jid.2014.468.

Abstract

Cutaneous T-cell lymphoma (CTCL) tumor cells lack the ability of activated T cells to undergo TCR/CD3-mediated activation-induced cell death (AICD). In this issue, the study reported by Wu et al. demonstrates that c-CBL (Casitas B-lineage Lymphoma proto-oncogene) is overexpressed in CTCL. When CTCL cells lose c-CBL, AICD is enhanced. Furthermore, combination therapy with methotrexate (a known demethylating agent for the CD95 gene) in combination with the loss of c-CBL increases CTCL cell death. Therefore, inhibition of c-CBL could represent a method of sensitizing lymphoma cells to enhance AICD. Armed with their novel data, the investigators envision combination therapies that target c-CBL to reactivate AICD in the malignant T cells whenever responsiveness to TCR/CD3 signaling is retained.

Publication types

  • Comment

MeSH terms

  • Apoptosis / drug effects*
  • Female
  • Gene Expression Regulation, Neoplastic / physiology*
  • Humans
  • Lymphoma, T-Cell, Cutaneous / metabolism*
  • Male
  • Proto-Oncogene Mas
  • Proto-Oncogene Proteins c-cbl / metabolism*
  • RNA, Small Interfering / pharmacology*
  • Skin Neoplasms / metabolism*
  • Up-Regulation / physiology*

Substances

  • MAS1 protein, human
  • Proto-Oncogene Mas
  • RNA, Small Interfering
  • Proto-Oncogene Proteins c-cbl
  • CBL protein, human