Study of pathogenesis in twitcher mouse, an enzymatically authentic model of human Krabbe's disease

J Inherit Metab Dis. 1989:12 Suppl 2:383-5. doi: 10.1007/BF03335429.
No abstract available

MeSH terms

  • Aging
  • Animals
  • Cerebrosides / biosynthesis*
  • Disease Models, Animal
  • Galactosylceramides / biosynthesis*
  • Leukodystrophy, Globoid Cell / physiopathology*
  • Mice
  • Mice, Neurologic Mutants / growth & development*
  • Sciatic Nerve / growth & development*
  • Sciatic Nerve / metabolism

Substances

  • Cerebrosides
  • Galactosylceramides