[Respiratory treatments in neuromuscular disease]

Abstract

In a previous article, a review was presented of the respiratory pathophysiology of the patient with neuromuscular disease, as well as their clinical evaluation and the major complications causing pulmonary deterioration. This article presents the respiratory treatments required to preserve lung function in neuromuscular disease as long as possible, as well as in special situations (respiratory infections, spinal curvature surgery, etc.). Special emphasis is made on the use of non-invasive ventilation, which is changing the natural history of many of these diseases. The increase in survival and life expectancy of these children means that they can continue their clinical care in adult units. The transition from pediatric care must be an active, timely and progressive process. It may be slightly stressful for the patient before the adaptation to this new environment, with multidisciplinary care always being maintained.

Keywords: Asistente de la tos; Atrofia muscular espinal; Chronic respiratory failure; Cough assist; Distrofia muscular de Duchenne; Duchenne muscular dystrophy; Enfermedad neuromuscular; Insuficiencia respiratoria crónica; Neumología pediátrica; Neuromuscular disease; Non-invasive ventilation; Pediatric respiratory medicine; Spinal muscular atrophy; Ventilación no invasiva.