PHACE syndrome: a retrospective review of 23 patients

Pediatr Dermatol. 2014 May-Jun;31(3):390-2. doi: 10.1111/pde.12304. Epub 2014 Mar 6.

Abstract

We present 23 patients with PHACE syndrome showing similarities in our population with data that already exist while highlighting neurodevelopmental occurrences arising in a subset of these patients.

MeSH terms

  • Adrenergic beta-Antagonists / administration & dosage
  • Adrenergic beta-Antagonists / adverse effects
  • Aortic Coarctation / drug therapy*
  • Aortic Coarctation / physiopathology*
  • Child
  • Child, Preschool
  • Eye Abnormalities / drug therapy*
  • Eye Abnormalities / physiopathology*
  • Female
  • Glucocorticoids / administration & dosage
  • Glucocorticoids / adverse effects
  • Humans
  • Infant
  • Infant, Newborn
  • Male
  • Nervous System / growth & development
  • Neurocutaneous Syndromes / drug therapy*
  • Neurocutaneous Syndromes / physiopathology*
  • Prednisolone / administration & dosage*
  • Prednisolone / adverse effects
  • Propranolol / administration & dosage*
  • Propranolol / adverse effects
  • Retrospective Studies
  • Treatment Outcome
  • Tubulin Modulators / administration & dosage
  • Tubulin Modulators / adverse effects
  • Vincristine / administration & dosage*
  • Vincristine / adverse effects

Substances

  • Adrenergic beta-Antagonists
  • Glucocorticoids
  • Tubulin Modulators
  • Vincristine
  • Prednisolone
  • Propranolol

Supplementary concepts

  • PHACE association