Sonic hedgehog signaling pathway mediates cerebrolysin-improved neurological function after stroke

Stroke. 2013 Jul;44(7):1965-72. doi: 10.1161/STROKEAHA.111.000831. Epub 2013 May 21.

Abstract

Background and purpose: Cerebrolysin, a mixture of neurotrophic peptides, enhances neurogenesis and improves neurological outcome in experimental neurodegenerative diseases and stroke. The Sonic hedgehog (Shh) signaling pathway stimulates neurogenesis after stroke. The present study tests whether the Shh pathway mediates cerebrolysin-induced neurogenesis and improves neurological outcome after stroke.

Methods: Rats subjected to embolic stroke were treated with cerebrolysin with or without cyclopamine.

Results: Using neural progenitor cells derived from the subventricular zone of the lateral ventricle of adult rats, we found that cerebrolysin significantly increased neural progenitor cells proliferation and their differentiation into neurons and myelinating oligodendrocytes, which were associated with upregulation of Shh and its receptors patched and smoothened. Blockage of the Shh signaling pathway with a pharmacological smoothened inhibitor, cyclopamine, abolished cerebrolysin-induced in vitro neurogenesis and oligodendrogenesis. In the ischemic rats, treatment with cerebrolysin starting 24 hours after stroke significantly increased neural progenitor cell proliferation in the subventricular zone and enhanced neurogenesis, oligodendrogenesis, and axonal remodeling in the peri-infarct area. Moreover, profound neurological function improvements were observed in rats treated with cerebrolysin from week 3 to week 5 after stroke onset compared with vehicle-treated rats. However, in vivo inhibition of the Shh pathway with cyclopamine completely reversed the effects of cerebrolysin on neurorestoration and functional recovery.

Conclusions: These results demonstrate that the Shh pathway mediates cerebrolysin-enhanced neurogenesis and white matter remodeling and improves functional recovery in rats after stroke.

Keywords: neurogenesis; recovery; stroke.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acids / administration & dosage
  • Amino Acids / pharmacology*
  • Animals
  • Antihypertensive Agents / administration & dosage
  • Antihypertensive Agents / pharmacology*
  • Cell Differentiation / drug effects
  • Cell Proliferation / drug effects*
  • Disease Models, Animal
  • Hedgehog Proteins / physiology*
  • Infarction, Middle Cerebral Artery / drug therapy*
  • Infarction, Middle Cerebral Artery / physiopathology
  • Male
  • Neurogenesis / drug effects
  • Neurogenesis / physiology
  • Neuroprotective Agents / administration & dosage
  • Neuroprotective Agents / pharmacology*
  • Patched Receptors
  • Random Allocation
  • Rats
  • Rats, Wistar
  • Receptors, Cell Surface / physiology*
  • Recovery of Function / physiology
  • Signal Transduction / drug effects
  • Signal Transduction / physiology*

Substances

  • Amino Acids
  • Antihypertensive Agents
  • Hedgehog Proteins
  • Neuroprotective Agents
  • Patched Receptors
  • Receptors, Cell Surface
  • Shh protein, rat
  • cerebrolysin