Epilepsy with cognitive deficit and autism spectrum disorders: prospective diagnosis by array CGH

Am J Med Genet B Neuropsychiatr Genet. 2013 Jan;162B(1):24-35. doi: 10.1002/ajmg.b.32114. Epub 2012 Nov 26.

Abstract

The clinical significance of chromosomal microdeletions and microduplications was predicted based on their gene content, de novo or familial inheritance and accumulated knowledge recorded on public databases. A patient group comprised of 247 cases with epilepsy and its common co-morbidities of developmental delay, intellectual disability, autism spectrum disorders, and congenital abnormalities was reviewed prospectively in a diagnostic setting using a standardized oligo-array CGH platform. Seventy-three (29.6%) had copy number variations (CNVs) and of these 73 cases, 27 (37.0%) had CNVs that were likely causative. These 27 cases comprised 10.9% of the 247 cases reviewed. The range of pathogenic CNVs associated with seizures was consistent with the existence of many genetic determinants for epilepsy.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Child
  • Child Development Disorders, Pervasive / complications*
  • Child Development Disorders, Pervasive / diagnosis*
  • Child Development Disorders, Pervasive / genetics
  • Child, Preschool
  • Chromosome Deletion
  • Chromosome Duplication / genetics
  • Cognition Disorders / complications*
  • Cognition Disorders / diagnosis*
  • Cognition Disorders / genetics
  • Comparative Genomic Hybridization*
  • DNA Copy Number Variations / genetics
  • Epilepsy / complications*
  • Epilepsy / diagnosis*
  • Epilepsy / genetics
  • Female
  • Genetic Counseling
  • Genetic Predisposition to Disease
  • Humans
  • Incidental Findings
  • Infant
  • Male
  • Middle Aged
  • Young Adult