Control of B cells expressing naturally occurring autoantibodies

Adv Exp Med Biol. 2012:750:145-56. doi: 10.1007/978-1-4614-3461-0_11.

Abstract

Naturally occurring autoantibodies (NAbs) are typically polyreactive, bind with low affinity to a discrete set of autoantigens and are encoded by variable region genes in germline configuration. They differ from disease-associated autoantibodies (autoAb), which are mostly monoreactive, somatically mutated and of high affinities. Structure-function studies have shown that polyreactivity of NAbs relies on the somatically generated complementarity determining region, CDR3, of the heavy chain. This finding suggested that NAb-producing B cells were positively selected from the pre-immune B-cell repertoire. The biological significance of this selection remains, however, unclear. Data originating mainly from transgenic mice have shown that mature NAb-producing B cells are frequently ignorant toward their antigen, possibly due to their low affinity, though active tolerance mechanisms are not excluded. An important issue is whether NAb-producing B cells constitute the pool from which pathologic auto Ab emerge after autoantigen-driven maturation. We summarize results obtained in mouse models, showing that some infectious agents are able to induce an autoantigen-driven activation of certain NAb-producing B cells. However direct proof that selection by autoantigen may lead to somatic hypermutation are still lacking. Other data tend to suggest that pathologic auto Abs may derive from non-autoimmune B cells that have diversified by somatic hypermutation of their variable region genes.

Publication types

  • Review

MeSH terms

  • Animals
  • Antibody Affinity
  • Antibody Specificity
  • Autoantibodies / classification
  • Autoantibodies / immunology*
  • Autoantigens / immunology
  • Autoimmunity*
  • B-Lymphocytes / cytology
  • B-Lymphocytes / immunology*
  • Communicable Diseases / immunology*
  • Complementarity Determining Regions / immunology
  • Humans
  • Immunoglobulin Variable Region / genetics
  • Immunoglobulin Variable Region / immunology
  • Mice
  • Mice, Transgenic
  • Mutation

Substances

  • Autoantibodies
  • Autoantigens
  • Complementarity Determining Regions
  • Immunoglobulin Variable Region