MAPT H1 haplotype is associated with enhanced α-synuclein deposition in dementia with Lewy bodies

Neurobiol Aging. 2013 Mar;34(3):936-42. doi: 10.1016/j.neurobiolaging.2012.06.015. Epub 2012 Jul 21.

Abstract

The microtubule-associated protein tau (MAPT) H1 haplotype has been identified as a genetic risk factor for synucleinopathies. However, whether it modulates tau or α-synuclein pathology remains unknown. Our aim was to investigate the relationship between MAPT haplotypes and pathologic aggregates of tau and α-synuclein in pathologically confirmed cases of dementia with Lewy bodies (DLB). Twenty-two cases fulfilling clinical and neuropathological criteria for DLB were included. Clinical and neuropathological data were collected, and APOE and MAPT genotypes were determined. Tau and α-synuclein pathology was assessed semiquantitatively in 17 brain areas and total scores were calculated. DLB H1/H1 (n = 12) and H2 carriers (n = 10) did not differ in demographics, clinical variables, concomitant Alzheimer's pathology, or APOE genotype. Total α-synuclein scores were significantly increased in the H1/H1 group (p = 0.011), largely due to an increase in brainstem regions. This difference was driven by an increase in Lewy bodies and diffuse and punctuate cytoplasmatic α-synuclein aggregates (p = 0.007 and p = 0.025 respectively). These findings provide a mechanistic link for the genetic association between MAPT haplotypes and synucleinopathies.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Aged, 80 and over
  • Apolipoprotein E4 / genetics
  • Brain / metabolism*
  • Female
  • Genetic Predisposition to Disease
  • Genotype
  • Haplotypes
  • Humans
  • Lewy Bodies / metabolism
  • Lewy Body Disease / genetics*
  • Lewy Body Disease / metabolism
  • Male
  • alpha-Synuclein / metabolism*
  • tau Proteins / genetics*

Substances

  • Apolipoprotein E4
  • MAPT protein, human
  • SNCA protein, human
  • alpha-Synuclein
  • tau Proteins