Mosaic amplification of multiple receptor tyrosine kinase genes in glioblastoma

Cancer Cell. 2011 Dec 13;20(6):810-7. doi: 10.1016/j.ccr.2011.11.005. Epub 2011 Dec 1.

Abstract

Tumor heterogeneity has been implicated in tumor growth and progression as well as resistance to therapy. We present an example of genetic heterogeneity in human malignant brain tumors in which multiple closely related driver genes are amplified and activated simultaneously in adjacent intermingled cells. We have observed up to three different receptor tyrosine kinases (EGFR, MET, PDGFRA) amplified in single tumors in different cells in a mutually exclusive fashion. Each subpopulation was actively dividing, and the genetic changes resulted in protein production, and coexisting subpopulations shared common early genetic mutations indicating their derivation from a single precursor cell. The stable coexistence of different clones within the same tumor will have important clinical implications for tumor resistance to targeted therapies.

MeSH terms

  • Adult
  • Aged
  • Base Sequence
  • Brain Neoplasms / genetics*
  • Brain Neoplasms / metabolism
  • Brain Neoplasms / pathology
  • Comparative Genomic Hybridization
  • DNA Copy Number Variations
  • ErbB Receptors / genetics*
  • ErbB Receptors / metabolism
  • Female
  • Genetic Heterogeneity
  • Glioblastoma / genetics*
  • Glioblastoma / metabolism
  • Glioblastoma / pathology
  • Humans
  • Male
  • Middle Aged
  • Mosaicism*
  • Proto-Oncogene Proteins c-met / genetics*
  • Proto-Oncogene Proteins c-met / metabolism
  • Receptor, Platelet-Derived Growth Factor alpha / genetics*
  • Receptor, Platelet-Derived Growth Factor alpha / metabolism

Substances

  • ErbB Receptors
  • MET protein, human
  • Proto-Oncogene Proteins c-met
  • Receptor, Platelet-Derived Growth Factor alpha

Associated data

  • GEO/GSE33483