ERIS, an endoplasmic reticulum IFN stimulator, activates innate immune signaling through dimerization

Proc Natl Acad Sci U S A. 2009 May 26;106(21):8653-8. doi: 10.1073/pnas.0900850106. Epub 2009 May 11.

Abstract

We report here the identification and characterization of a protein, ERIS, an endoplasmic reticulum (ER) IFN stimulator, which is a strong type I IFN stimulator and plays a pivotal role in response to both non-self-cytosolic RNA and dsDNA. ERIS (also known as STING or MITA) resided exclusively on ER membrane. The ER retention/retrieval sequence RIR was found to be critical to retain the protein on ER membrane and to maintain its integrity. ERIS was dimerized on innate immune challenges. Coumermycin-induced ERIS dimerization led to strong and fast IFN induction, suggesting that dimerization of ERIS was critical for self-activation and subsequent downstream signaling.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cell Line
  • Endoplasmic Reticulum / immunology
  • Endoplasmic Reticulum / metabolism
  • Humans
  • Immunity, Innate / immunology*
  • Membrane Proteins / immunology*
  • Membrane Proteins / metabolism
  • Mice
  • Protein Multimerization / immunology*
  • Signal Transduction / immunology*
  • Up-Regulation / immunology

Substances

  • CISD2 protein, human
  • Membrane Proteins