IRF4 is essential for IL-21-mediated induction, amplification, and stabilization of the Th17 phenotype

Proc Natl Acad Sci U S A. 2008 Dec 30;105(52):20846-51. doi: 10.1073/pnas.0809077106. Epub 2008 Dec 16.

Abstract

Differentiation of murine T-helper (Th) 17 cells is induced by antigenic stimulation and the sequential action of the cytokines IL-6, IL-21, and IL-23, along with TGFbeta. Current dogma proposes that IL-6 induces IL-21, which, in a STAT3-dependent manner, amplifies its own transcription, contributes to IL-17 production, and, moreover, promotes the expression of the IL-23 receptor. This, in turn, prepares cells for IL-23-mediated stabilization of the Th17 phenotype. Here we demonstrate that these effects of IL-21 on Th17 differentiation are completely dependent on IFN regulatory factor 4 (IRF4). After culturing in the presence of IL-21 plus TGFbeta, IRF4-deficient (Irf4(-/-)) Th cells showed a profound intrinsic defect in IL-17 production and in the autocrine IL-21 loop. Likewise, the levels of IL-23 receptor and the lineage-specific orphan nuclear receptors RORalpha and RORgammat were diminished, whereas the T regulatory (Treg) transcription factor forkhead box P3 (Foxp3) was strongly up-regulated, consistent with the reciprocal relationship between Th17 and Treg development. Despite this loss of IL-21 functions, IL-21-induced STAT3 activation was unimpaired and induced normal Socs3 expression. Forced expression of Foxp3 in WT cells inhibited IL-21-mediated IL-17 production, suggesting that the increase in Foxp3 contributes to the Irf4(-/-) phenotype. Additionally, the low levels of RORalpha and RORgammat are also partially responsible, because simultaneous overexpression of both proteins restored IL-17 production in Irf4(-/-) cells to some extent. These data highlight IRF4 as a decisive factor during the IL-21-mediated steps of Th17 development by influencing the balance of Foxp3, RORalpha, and RORgammat.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Autocrine Communication / immunology*
  • Cells, Cultured
  • Cytokines / genetics
  • Cytokines / immunology
  • Forkhead Transcription Factors / genetics
  • Forkhead Transcription Factors / immunology
  • Interferon Regulatory Factors / genetics
  • Interferon Regulatory Factors / immunology*
  • Interleukins / genetics
  • Interleukins / immunology*
  • Mice
  • Mice, Knockout
  • Nuclear Receptor Subfamily 1, Group F, Member 1
  • Nuclear Receptor Subfamily 1, Group F, Member 3
  • Phenotype
  • Receptors, Cytoplasmic and Nuclear / genetics
  • Receptors, Cytoplasmic and Nuclear / immunology
  • Receptors, Interleukin / genetics
  • Receptors, Interleukin / immunology
  • Receptors, Retinoic Acid / genetics
  • Receptors, Retinoic Acid / immunology
  • Receptors, Thyroid Hormone / genetics
  • Receptors, Thyroid Hormone / immunology
  • STAT3 Transcription Factor / genetics
  • STAT3 Transcription Factor / immunology
  • T-Lymphocytes, Helper-Inducer / immunology*
  • Trans-Activators / genetics
  • Trans-Activators / immunology
  • Up-Regulation / immunology

Substances

  • Cytokines
  • Forkhead Transcription Factors
  • Foxp3 protein, mouse
  • Interferon Regulatory Factors
  • Interleukins
  • Nuclear Receptor Subfamily 1, Group F, Member 1
  • Nuclear Receptor Subfamily 1, Group F, Member 3
  • Receptors, Cytoplasmic and Nuclear
  • Receptors, Interleukin
  • Receptors, Retinoic Acid
  • Receptors, Thyroid Hormone
  • Rorc protein, mouse
  • STAT3 Transcription Factor
  • Stat3 protein, mouse
  • Trans-Activators
  • interferon regulatory factor-4
  • interleukin-23 receptor, mouse
  • interleukin-21