Qualitative evidence of Ri specific IgG-synthesis in the cerebrospinal fluid from patients with paraneoplastic neurological syndromes

J Neurol Sci. 2008 May 15;268(1-2):65-8. doi: 10.1016/j.jns.2007.11.002. Epub 2007 Dec 21.

Abstract

The presence of Ri-specific oligoclonal IgG bands in the CSF was investigated in five patients with paraneoplastic anti-Ri associated neurological syndromes (PNS) and six controls. In 4/5 CSF samples reactivity of IgG bands with recombinant Ri antigen was found using isoelectrofocusing combined with affinity blotting; in one patient with absence of oligoclonal bands of total IgG in CSF Ri-specific oligoclonal bands were detected with the same sample, indicating a higher sensitivity of Ri-specific affinity blotting as compared to affinity blotting with anti-human IgG antibodies. Our results confirm previous studies demonstrating IgG synthesis against onconeuronal antigens by intrathecal B-cell clones in PNS and extend this observation to patients with anti-Ri syndrome. The pathogenic relevance of these antibodies, however, is further challenged by the finding that specific intrathecal IgG synthesis might not be a prerequisite of CNS involvement, because it was missed in one of our patients.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Antigens, Neoplasm / immunology*
  • Female
  • Humans
  • Isoelectric Focusing / methods
  • Male
  • Middle Aged
  • Nerve Tissue Proteins / immunology*
  • Neuro-Oncological Ventral Antigen
  • Oligoclonal Bands / cerebrospinal fluid*
  • Paraneoplastic Polyneuropathy / cerebrospinal fluid*
  • RNA-Binding Proteins / immunology*

Substances

  • Antigens, Neoplasm
  • Nerve Tissue Proteins
  • Neuro-Oncological Ventral Antigen
  • Oligoclonal Bands
  • RNA-Binding Proteins