Variation in Niemann-Pick C1-like 1 gene as a determinant of apolipoprotein B-100 kinetics and response to statin therapy in centrally obese men

Clin Endocrinol (Oxf). 2008 Jul;69(1):45-51. doi: 10.1111/j.1365-2265.2007.03144.x. Epub 2008 Jul 1.

Abstract

Objective: Niemann-Pick C1-like 1 protein (NPC1L1) plays a key role in lipoprotein metabolism. We examined the association of common genetic polymorphisms in NPC1L1 on apolipoprotein (apo) B-100 metabolism and the response to statin treatment in 37 men with central obesity.

Research methods and procedure: Very-low density lipoprotein (VLDL) and low-density lipoprotein (LDL)-apoB kinetics were determined using stable isotope method. NPC1L1 genotypes (1735G > C, 25432A > C and 27677T > C) were determined by allele-specific methods. These three polymorphisms are defined as haplotype, namely 1735C-25432A-27677T, and was designated as 'haplotype 2'.

Results: Relative to non-2/2 haplotype (n = 23), subjects with the 2/2 haplotype (n = 14) had significantly increased plasma concentrations of total, LDL-cholesterol, and total apoB (P < 0.05). The fractional catabolic rate (FCR) of LDL-apoB was significantly lower in 2/2 subjects compared with non-2/2 subjects (P < 0.05), with an associated increase in LDL-apoB pool size in the former group. Sixteen subjects were then treated with 40 mg atorvastatin (6 weeks): 2/2 subjects (n = 8) had a significantly greater reduction in plasma concentrations of cholesterol and total apoB and in LDL-apoB pool size, as well as a greater increase in LDL-apoB FCR compared with non-2/2 subjects. There were no significant treatment-related between-haplotype differences in VLDL-apoB kinetics or in plasma concentrations of lathosterol and campesterol.

Conclusion: Our data demonstrate that NPC1L1 2/2 haplotype was associated with variation in LDL-apoB metabolism and its response to statin therapy in centrally obese men, by a mechanism that did not involve changes in VLDL-apoB kinetics, nor cholesterol synthesis or absorption.

Publication types

  • Clinical Trial
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Anti-Obesity Agents / therapeutic use
  • Apolipoprotein B-100 / blood
  • Apolipoprotein B-100 / metabolism*
  • Atorvastatin
  • Cholesterol, VLDL / blood
  • Cholesterol, VLDL / metabolism
  • Drug Resistance / genetics
  • Genetic Variation / physiology
  • Genotype
  • Heptanoic Acids / therapeutic use
  • Humans
  • Hydroxymethylglutaryl-CoA Reductase Inhibitors / therapeutic use*
  • Kinetics
  • Male
  • Membrane Proteins / genetics*
  • Membrane Transport Proteins
  • Middle Aged
  • Obesity / blood
  • Obesity / drug therapy*
  • Obesity / genetics*
  • Obesity / metabolism
  • Pyrroles / therapeutic use
  • Treatment Outcome

Substances

  • Anti-Obesity Agents
  • Apolipoprotein B-100
  • Cholesterol, VLDL
  • Heptanoic Acids
  • Hydroxymethylglutaryl-CoA Reductase Inhibitors
  • Membrane Proteins
  • Membrane Transport Proteins
  • NPC1L1 protein, human
  • Pyrroles
  • Atorvastatin