Determinants of oncogenic transformation in acute promyelocytic leukemia: the hetero-union makes the force

Cancer Cell. 2007 Jul;12(1):1-3. doi: 10.1016/j.ccr.2007.06.012.

Abstract

Acute promyelocytic leukemia (APL) is caused by chromosomal translocations that involve the retinoic acid receptor alpha (RAR) and several other genes to yield X-RAR fusion proteins. Unlike wild-type RARs, which require heterodimerization with the retinoid X receptor (RXR) for their function as DNA-binding transcriptional regulators, X-RAR fusion proteins bind DNA and deregulate transcription as homo-oligomers. In this issue of Cancer Cell, however, Zeisig et al. and Zhu et al. show that RXR recruitment is a critical determinant for the transforming potential of oligomeric X-RAR fusion proteins and explore the possibility for targeted interventions in APL with either RAR or RXR ligands.

Publication types

  • Comment
  • Review

MeSH terms

  • Cell Transformation, Neoplastic*
  • Humans
  • Leukemia, Promyelocytic, Acute / pathology*
  • Ligands
  • Receptors, Retinoic Acid / metabolism
  • Retinoid X Receptors / metabolism

Substances

  • Ligands
  • Receptors, Retinoic Acid
  • Retinoid X Receptors