Neonatal epithelioid sarcoma: a distinct clinical entity?

J Pediatr Surg. 2006 Jul;41(7):e9-e11. doi: 10.1016/j.jpedsurg.2006.03.014.

Abstract

Epithelioid sarcoma is a rare soft tissue sarcoma with a propensity for local aggressiveness, regional nodal spread, and pulmonary metastases. We report a case of epithelioid sarcoma in a neonate with bilateral optic nerve hypoplasia who developed liver, kidney, and bone metastases. The unusual presenting features and pattern of disease progression in this patient suggest that a different disease evaluation strategy should be considered for infants with epithelioid sarcoma.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Forearm
  • Humans
  • Infant, Newborn
  • Kidney Neoplasms / diagnosis
  • Kidney Neoplasms / secondary*
  • Kidney Neoplasms / surgery
  • Liver Neoplasms / diagnosis
  • Liver Neoplasms / secondary*
  • Liver Neoplasms / surgery
  • Neoplasm Metastasis
  • Neoplasm Recurrence, Local*
  • Sarcoma / diagnosis
  • Sarcoma / secondary*
  • Sarcoma / surgery
  • Soft Tissue Neoplasms / diagnosis
  • Soft Tissue Neoplasms / pathology*
  • Soft Tissue Neoplasms / surgery
  • Thigh