[Prenatal diagnosis of prelingual deafness by determination of SLC26A4 gene mutation]

Zhonghua Fu Chan Ke Za Zhi. 2005 Sep;40(9):591-4.
[Article in Chinese]

Abstract

Objective: To identify deafness related gene and provide its prenatal diagnosis to avoid deaf fetus delivery.

Methods: DNA was extracted from amniotic cells in a pregnant woman close to 21 weeks' gestation, as well as from peripheral blood cells of the pregnant woman, her husband and their two sons. Screening for GJB2 and SLC26A4 gene mutations was firstly performed in the deafness proband (the first son of the couple), and then it was carried out in the fetus and the rest family members.

Results: The first child of the family, i.e., the proband, was homozygous in the IVS7-2A > G mutation of SLC26A4, the parents and the second child were carriers of the same mutation, while the fetus had a wild-type form.

Conclusion: It is feasible to identify deafness related genes by screening for GJB2 and SLC26A4 mutation, thus providing correct prenatal diagnosis and avoiding deaf delivery of baby.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Base Sequence
  • Child
  • Connexin 26
  • Connexins
  • DNA Mutational Analysis
  • Deafness / diagnosis*
  • Deafness / genetics*
  • Female
  • Fetal Diseases / diagnosis
  • Fetal Diseases / genetics
  • Humans
  • Infant
  • Male
  • Membrane Transport Proteins / genetics*
  • Mutation*
  • Pedigree
  • Polymerase Chain Reaction
  • Pregnancy
  • Prenatal Diagnosis
  • Sulfate Transporters

Substances

  • Connexins
  • GJB2 protein, human
  • Membrane Transport Proteins
  • SLC26A4 protein, human
  • Sulfate Transporters
  • Connexin 26