Targeting the JNK pathway as a therapeutic protective strategy for nervous system diseases

Rev Neurosci. 2005;16(1):57-67. doi: 10.1515/revneuro.2005.16.1.57.

Abstract

The c-Jun N-terminal kinases (JNKs) are members of the family of mitogen activated protein kinases (MAPKs). While the functions of the JNKs under physiological conditions are diverse and not completely understood, there is increasing evidence that JNKs are potent effectors of apoptosis in both the brain and the mammalian inner ear following a variety of injuries. The activation of the inducible transcription factor c-Jun by N-terminal phosphorylation is a central event in JNK-mediated neural and inner ear hair cell death. A cell permeable peptide designed specifically to inhibit JNK signaling has proven successful in in vivo models of both neuronal degeneration following cerebral ischemia and auditory hair cell degeneration following exposure to either acoustic trauma or a toxic level of an aminoglycoside antibiotic. Here we discuss the evidence supporting the application of JNK inhibitors to prevent cellular degeneration in several central nervous system (CNS) and peripheral nervous system (PNS) diseases with an emphasis on traumatic ischemic damage to the CNS and acquired deafness in the PNS receptors.

Publication types

  • Review

MeSH terms

  • Animals
  • Brain Ischemia / drug therapy
  • Brain Ischemia / enzymology
  • Brain Ischemia / physiopathology
  • Deafness / drug therapy
  • Deafness / enzymology
  • Deafness / physiopathology
  • Hair Cells, Auditory / drug effects
  • Hair Cells, Auditory / enzymology
  • Hair Cells, Auditory / physiopathology
  • Humans
  • JNK Mitogen-Activated Protein Kinases / drug effects
  • JNK Mitogen-Activated Protein Kinases / metabolism*
  • Nerve Degeneration / drug therapy*
  • Nerve Degeneration / enzymology*
  • Nerve Degeneration / prevention & control
  • Nervous System Diseases / drug therapy*
  • Nervous System Diseases / enzymology*
  • Nervous System Diseases / physiopathology
  • Neuroprotective Agents / chemistry
  • Neuroprotective Agents / pharmacology*
  • Neurotoxicity Syndromes / drug therapy
  • Neurotoxicity Syndromes / enzymology
  • Neurotoxicity Syndromes / physiopathology
  • Signal Transduction / drug effects
  • Signal Transduction / physiology

Substances

  • Neuroprotective Agents
  • JNK Mitogen-Activated Protein Kinases