Functional effect of the R110Q IL13 genetic variant alone and in combination with IL4RA genetic variants

J Allergy Clin Immunol. 2004 Sep;114(3):553-60. doi: 10.1016/j.jaci.2004.04.044.

Abstract

Background: IL-13 is a key mediator of allergic asthma. IL-13 mediates its effects via its receptor, a heterodimer composed of IL-4R alpha and IL-13R alpha1. Polymorphic variants of both IL-13 and IL-4R alpha have been shown to be associated with atopy.

Objective: We examined the functional consequences of the Q110 IL-13 variant in vitro and in vivo to determine whether it displays enhanced functional activity compared with R110 IL-13, both in the context of I50Q551 IL-4R alpha and of the atopy-associated variant V50R551 IL-4R alpha.

Methods: We used a mouse cell line stably expressing human IL-4R alpha and IL-13R alpha1 that readily responds to human IL-4 and IL-13. For in vivo analyses, we used BALB/c mice.

Results: The Q110 IL-13 variant displayed significantly increased activity compared with R110 IL-13. Furthermore, mice treated with Q110 IL-13 variant displayed increased airways hyperresponsiveness relative to R110 IL-13. We then examined the functional consequences of Q110 IL-13 variant in combination with an atopy-associated variant of its receptor, IL-4R alpha (V50R551). Q110 IL-13 variant had increased activity on these cells as well, and, strikingly, the effect was greater than that observed in cells expressing I50Q551 IL-4R alpha.

Conclusion: Either Q110 IL-13 variant or V50R551 IL-4R alpha variant has enhanced function alone, but the 2 together have a synergistic effect on IL-13-dependent gene induction. Our data demonstrate the importance of relatively small individual differences in gene products from common single nucleotide polymorphisms that may result in larger combined differences. Furthermore, a relatively modest change in function from a single nucleotide polymorphism can result in an important biological difference in vivo.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Asthma / genetics
  • Asthma / immunology
  • B-Lymphocytes
  • Cell Line
  • Genetic Variation*
  • Humans
  • Hypersensitivity, Immediate / genetics
  • Hypersensitivity, Immediate / immunology
  • Interleukin-13 / genetics*
  • Mice
  • Mice, Inbred BALB C
  • Polymorphism, Single Nucleotide
  • Receptors, Interleukin-4 / genetics*
  • Signal Transduction
  • Transfection

Substances

  • Interleukin-13
  • Receptors, Interleukin-4