Short- and long-term results of liver transplantation in infants aged less than 6 months

Transplantation. 2004 Jul 27;78(2):235-41. doi: 10.1097/01.tp.0000128189.54868.18.

Abstract

Background: Despite major surgical and medical advances, it is still a challenge to perform transplantation in small infants. This study, focusing on short- and long-term outcomes, summarizes our 10-year experience with liver transplantation (LTx) in infants aged less than 6 months.

Patients and methods: We analyzed 43 patients aged 6 months or less (range: 12-184 days, median: 136 days) whose median weight at the time of LTx was 5.8 kg (range: 2.8-8.0 kg). The reasons for LTx were biliary atresia (n=27; 62.8%), neonatal hepatitis (n=6; 14%), neonatal cholestasis (n=4; 9.3%), and miscellaneous (n=6; 14%). The patients were followed up for a median time of 3 years and evaluated with respect to graft function, physical, and neurodevelopmental outcome.

Results: The patient survival was 90.7% after 1 year and 87.2% after 2 years. The graft survival was 86% after 1 year and 82.1% after 2 years. Twelve patients (27.9%) experienced 15 surgical complications requiring intervention, two of whom demonstrated vascular thrombosis (4.7%). Acute early rejection occurred in 15 patients (34.9%), and chronic rejection occurred in 3 patients (7%); 83.3% of the patients had normal liver function test results at the time of evaluation. Complications such as posttransplant lymphoproliferative disease (4.7%) and persistent arterial hypertension (4.7%) were rarely seen. The physical and neurodevelopmental outcomes were good.

Conclusions: LTx in infants aged less than 6 months provides excellent short- and long-term results. Low weight or young age of infants awaiting LTx should not be exclusion criteria for LTx.

MeSH terms

  • Body Weight
  • Cyclosporine / therapeutic use
  • Drug Administration Schedule
  • Female
  • Follow-Up Studies
  • Graft Rejection / epidemiology
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Infant
  • Infant, Newborn
  • Infections / epidemiology
  • Liver Diseases / classification
  • Liver Diseases / surgery
  • Liver Transplantation / mortality
  • Liver Transplantation / physiology*
  • Male
  • Methylprednisolone / therapeutic use
  • Postoperative Complications / classification
  • Postoperative Complications / epidemiology
  • Retrospective Studies
  • Survival Analysis
  • Time Factors
  • Treatment Outcome

Substances

  • Immunosuppressive Agents
  • Cyclosporine
  • Methylprednisolone