The microsomal triglyceride transfer protein gene-493T variant lowers cholesterol but increases the risk of coronary heart disease

Circulation. 2004 May 18;109(19):2279-84. doi: 10.1161/01.CIR.0000130070.96758.7b. Epub 2004 May 10.

Abstract

Background: The microsomal triglyceride transfer protein (MTP) transfers lipids into apolipoprotein B-containing lipoproteins for secretion from liver, intestine, and heart. The T-variant of a functional polymorphism in the MTP promoter, MTP-493G/T, has been associated with reduced low-density lipoprotein cholesterol concentrations. We hypothesize that this polymorphism impacts on coronary heart disease (CHD) risk.

Methods and results: The effect of the polymorphism was therefore tested in the West of Scotland Coronary Prevention Study biobank (580 cases and 1160 controls). MTP-493T carrier status was associated with significantly increased risk of CHD despite a small reduction in total cholesterol. Compared with the genotypic group with the lowest event rate (MTP-493GG, pravastatin treatment), the respective odds ratios (95% confidence interval) in the placebo group for CHD events were: GG, 1.23 (0.92 to 1.63); GT, 1.53 (1.12 to 2.08); and TT, 2.78 (1.53 to 5.05), suggestive of a gene-dose effect. The excess risk for CHD of the MTP-493T-variant was eliminated by pravastatin treatment. The Uppsala Longitudinal Study of Adult Men (ULSAM), which is a 20-year follow-up study of CHD, was used as an independent confirmatory database. These unexpected findings prompted the investigation of non-plasma lipid factors that could associate the MTP gene with CHD risk. In a limited number of subjects (n=18), heart muscle biopsies showed a MTP-493T genotype-specific depression of MTP mRNA expression.

Conclusions: The MTP-493T variant confers an increased risk of CHD that is unrelated to plasma lipids and lipoproteins, but eliminated by pravastatin treatment. A direct effect of the MTP polymorphism on myocardial lipid metabolism and vulnerability upon ischemic damage cannot be excluded.

Publication types

  • Clinical Trial
  • Multicenter Study
  • Randomized Controlled Trial
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Abetalipoproteinemia
  • Anticholesteremic Agents / therapeutic use
  • Biopsy
  • Carrier Proteins / genetics*
  • Case-Control Studies
  • Cholesterol, LDL / deficiency
  • Codon / genetics
  • Cohort Studies
  • Coronary Disease / blood
  • Coronary Disease / epidemiology*
  • Coronary Disease / genetics
  • Disease Susceptibility
  • Double-Blind Method
  • Genotype
  • Haplotypes / genetics
  • Humans
  • Hydroxymethylglutaryl-CoA Reductase Inhibitors / therapeutic use
  • Lipid Metabolism
  • Lipoproteins / metabolism
  • Longitudinal Studies
  • Male
  • Middle Aged
  • Myocardial Infarction / epidemiology
  • Myocardium / metabolism
  • Myocardium / pathology
  • Polymorphism, Genetic*
  • Pravastatin / therapeutic use
  • Promoter Regions, Genetic / genetics*
  • Prospective Studies
  • RNA, Messenger / biosynthesis
  • Risk
  • Scotland / epidemiology
  • Sweden / epidemiology

Substances

  • Anticholesteremic Agents
  • Carrier Proteins
  • Cholesterol, LDL
  • Codon
  • Hydroxymethylglutaryl-CoA Reductase Inhibitors
  • Lipoproteins
  • RNA, Messenger
  • microsomal triglyceride transfer protein
  • Pravastatin