Fibrillin 1 abnormalities in dermal fibroblast cultures from first-degree relatives of patients with systemic sclerosis (scleroderma)

Arthritis Rheum. 2004 Jan;50(1):329-32. doi: 10.1002/art.11437.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adult
  • Aged
  • Cells, Cultured
  • Dermis / pathology
  • Female
  • Fibrillin-1
  • Fibrillins
  • Fibroblasts / pathology
  • Fibroblasts / physiology
  • Humans
  • Male
  • Microfibrils / pathology
  • Microfilament Proteins / genetics*
  • Microfilament Proteins / metabolism
  • Middle Aged
  • Phenotype
  • Scleroderma, Systemic / genetics*
  • Scleroderma, Systemic / pathology

Substances

  • FBN1 protein, human
  • Fibrillin-1
  • Fibrillins
  • Microfilament Proteins