Post-induction residual disease in translocation t(12;21)-positive childhood ALL

Med Pediatr Oncol. 2003 Feb;40(2):82-7. doi: 10.1002/mpo.10217.

Abstract

Background: t(12;21)(p1 3;q22), the most frequent chromosomal translocation found in childhood acute lymphoblastic leukemia (ALL), occurs in approximately 25% of B-lineage ALL cases and has been claimed to carry a good prognosis.

Procedure: As part of the Nordic Society of Pediatric Hematology and Oncology (NOPHO) ALL-MRD 95 study, which includes children from Iceland, Norway, and Denmark diagnose d with ALL, patients were screened for the presence of t(12; 21) by reverse transcriptase-polymerase chain reaction (RT-PCR) at diagnosis, and their residual disease was quantified after 4 weeks of induction therapy (prednisolone, vincristine, doxorubicin, i.t. methotrexate) by a competitive, clone-specific, semi-nested PCR analysis.

Results: Among 96 children diagnosed with ALL, and quantified for post induction residual disease, 32 were t(12;21)-positive. The median residual disease was similar for B-precursor ALL patients with and without t(12;21) (0.009 vs. 0.03%, P = 0.12).

Conclusions: Al though patients with t(12;21)-positive ALL have been claimed to have a good outcome, these data indicate that this does not reflect a high sensitivity to prednisolone, vincristine, and doxorubicin given during induction therapy.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use*
  • Child
  • Child, Preschool
  • Chromosomes, Human, Pair 12 / genetics*
  • Chromosomes, Human, Pair 21 / genetics*
  • Core Binding Factor Alpha 2 Subunit
  • DNA Primers / chemistry
  • Doxorubicin / administration & dosage
  • Female
  • Humans
  • Immunophenotyping
  • Infant
  • Male
  • Methotrexate / administration & dosage
  • Neoplasm, Residual / drug therapy
  • Neoplasm, Residual / genetics*
  • Neoplasm, Residual / pathology
  • Oncogene Proteins, Fusion / genetics
  • Oncogene Proteins, Fusion / metabolism
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / drug therapy
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / genetics*
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / pathology
  • Prednisolone / administration & dosage
  • RNA, Messenger / metabolism
  • RNA, Neoplasm / metabolism
  • Remission Induction
  • Reverse Transcriptase Polymerase Chain Reaction
  • Translocation, Genetic*
  • Vincristine / administration & dosage

Substances

  • Core Binding Factor Alpha 2 Subunit
  • DNA Primers
  • Oncogene Proteins, Fusion
  • RNA, Messenger
  • RNA, Neoplasm
  • TEL-AML1 fusion protein
  • Vincristine
  • Doxorubicin
  • Prednisolone
  • Methotrexate