[alpha]-Secretase ADAM10 as well as [alpha]APPs is reduced in platelets and CSF of Alzheimer disease patients

Mol Med. 2002 Feb;8(2):67-74.

Abstract

Background: Members of membrane-bound disintegrin metalloproteinases (ADAMs) were shown to be capable of cleaving amyloid precursor protein (APP) at the alpha-cleavage site in different cell systems. One of the candidate alpha-secretases identified in this family is ADAM10. The present study addresses the following major questions: 1) Are the levels of an alpha-secretase candidate (i.e., ADAM10) reduced in accessible cells of Alzheimer Disease (AD) patients? 2) Are ADAM10 levels in the peripheral cells of AD patients related to a concomitant decrease in alpha APPs?

Materials and methods: Western Blot analysis of ADAM10 is performed on platelet homogenates from 33 sporadic AD patients and on 26 age-matched control subjects. Moreover, the levels of alpha-secretase metabolite (alpha APPs) are tested both in platelets and cerebrospinal fluid (CSF) of the same pool of subjects by means of Western blot with a specific antibody.

Results: A significant decrease of platelet ADAM10 levels is observed in patients affected by probable AD when compared to control subjects and this is paralleled by a reduced level of alpha APPs released from platelets. Moreover, in the same pool of AD patients, alpha APPs levels were reduced concomitantly in CSF.

Conclusions: ADAM10 is expressed in platelets. A reduced level of ADAM10 is observed in platelets obtained from AD patients compared to age-matched controls. Further, in the same pool of AD patients, a qualitatively and quantitatively similar decrease in alpha APPs is present both in thrombin-activated platelets and CSF, thus suggesting that alterations of APP processing might occur both in the neuronal compartment and peripheral cells.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • ADAM Proteins
  • ADAM10 Protein
  • Aged
  • Alzheimer Disease / blood*
  • Alzheimer Disease / cerebrospinal fluid*
  • Alzheimer Disease / metabolism
  • Amyloid Precursor Protein Secretases
  • Amyloid beta-Protein Precursor / analysis
  • Amyloid beta-Protein Precursor / blood*
  • Amyloid beta-Protein Precursor / cerebrospinal fluid*
  • Blood Platelets / chemistry
  • Blotting, Western
  • Cerebral Cortex / chemistry
  • Electrophoresis, Polyacrylamide Gel
  • Female
  • Glycosylation
  • Humans
  • Male
  • Matched-Pair Analysis
  • Membrane Proteins / analysis
  • Membrane Proteins / blood*
  • Membrane Proteins / cerebrospinal fluid*
  • Metalloendopeptidases / analysis
  • Metalloendopeptidases / blood*
  • Metalloendopeptidases / cerebrospinal fluid*
  • Middle Aged
  • Peptide Fragments / analysis
  • Peptide Fragments / blood*
  • Peptide Fragments / cerebrospinal fluid*
  • Platelet Activation
  • Precipitin Tests

Substances

  • APP protein, human
  • Amyloid beta-Protein Precursor
  • Membrane Proteins
  • Peptide Fragments
  • Amyloid Precursor Protein Secretases
  • ADAM Proteins
  • Metalloendopeptidases
  • ADAM10 Protein
  • ADAM10 protein, human