Twenty-four hour 17-hydroxyprogesterone response to adrenocorticotropine in adrenal incidentalomas: augmented response after adrenalectomy in two patients

Endocr J. 2002 Feb;49(1):35-40. doi: 10.1507/endocrj.49.35.

Abstract

The current study aimed to investigate the midterm (24 hour) response of 17-hydroxyprogesterone (17-OHP) and dehydroepiandrosterone sulphate (DHEA-S) to synthetic high-dose adrenocorticotropin (ACTH) in adrenal incidentalomas (Al). Seventeen patients with Al and 40 age- and sex-matched controls received synthetic ACTH (tetracosactide, 1000 microg, IM). Plasma, 17-OHP and DHEA-S were collected in basal conditions and after 1, 4, 6, 8 and 24 hours. (HPA) axis was also evaluated using circadian serum cortisol, urinary free cortisol and over-night 2 mg dexamethasone suppression. Basal plasma 17-OHP levels did not differ among the groups. However, the increment in plasma 17-OHP in patients both in terms of peak [13.76 +/- 2.52, 4.77 +/- 0.30ng/ml, mean +/- S.E.M, p < 0.001] and area under the curve [190 +/- 46, 96.75 +/- 32 ng/ml/h, p < 0.001] were significantly higher than that of the controls. Stimulated 17OH-P levels never reached 9.1 ng/ml in controls. Sixty-five (11/17) % of the patients were found to have exaggerated response. Three of the patients were found to have subclinical Cushing's syndrome and interestingly, two augmented their 17-OHP response to ACTH after unilateral adrenalectomy and normalisation of their HPA axis. Basal DHEA-S levels of the patients were significantly lower [99.21 +/- 45, 230.18 +/- 34 microg/dl, p < 0.01] and stayed persistently lower than that of the controls. Evidence of a heterozygous 21 hydroxylase deficiency, as indicated by the exaggerated 17-OHP response to ACTH, has been widely reported in Al patients. However, to our knowledge to date there is no report on augmented 17-OHP response to ACTH after adrenalectomy. Possible reasons for the augmentation were discussed.

Publication types

  • Case Reports

MeSH terms

  • 17-alpha-Hydroxyprogesterone / blood
  • 17-alpha-Hydroxyprogesterone / metabolism*
  • Adrenal Gland Neoplasms / drug therapy
  • Adrenal Gland Neoplasms / metabolism*
  • Adrenal Gland Neoplasms / surgery
  • Adrenalectomy
  • Adrenocorticotropic Hormone / pharmacokinetics
  • Adrenocorticotropic Hormone / pharmacology*
  • Adult
  • Aged
  • Area Under Curve
  • Case-Control Studies
  • Catecholamines / urine
  • Circadian Rhythm
  • Dehydroepiandrosterone Sulfate / blood
  • Dehydroepiandrosterone Sulfate / metabolism
  • Female
  • Humans
  • Hydrocortisone / blood
  • Hydrocortisone / urine
  • Male
  • Middle Aged
  • Statistics, Nonparametric
  • Vanilmandelic Acid / urine

Substances

  • Catecholamines
  • Vanilmandelic Acid
  • Dehydroepiandrosterone Sulfate
  • 17-alpha-Hydroxyprogesterone
  • Adrenocorticotropic Hormone
  • Hydrocortisone